Atormac
brintellex
Neurology India
menu-bar5 Open access journal indexed with Index Medicus
  Users online: 1131  
 Home | Login 
About Editorial board Articlesmenu-bullet NSI Publicationsmenu-bullet Search Instructions Online Submission Subscribe Videos Etcetera Contact
  Navigate Here 
    Next article
    Previous article
    Table of Contents

 Resource Links
    Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
    Citation Manager
    Access Statistics
    Reader Comments
    Email Alert *
    Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed1437    
    Printed74    
    Emailed0    
    PDF Downloaded0    
    Comments [Add]    

Recommend this journal

 

 
Year : 1997  |  Volume : 45  |  Issue : 1  |  Page : 9--13

Early onset cerebellar ataxia with retained tendon reflexes comparison with Friedreich's ataxia and olivopontocerebellar atrophy : an evoked potential study.


Department of Neurology, National Institute of Mental Health and Neuro Sciences (NIMHANS), Bangalore - 560 029, India

Correspondence Address:
PK Pal
Department of Neurology, National Institute of Mental Health and Neuro Sciences (NIMHANS), Bangalore - 560 029
India
Login to access the Email id

Source of Support: None, Conflict of Interest: None


PMID: 29509152

Rights and PermissionsRights and Permissions

14 patients with the clinical diagnosis of early onset cerebellar ataxia with retained tendon reflexes (EOCA) were evaluated by multimodal evoked potential (EP) studies. The results were compared with observations made on 10 patients with Friedreich's ataxia (FA) and 16 patients with olivopontocerebellar atrophy (OPCA). Ten patients (71.4) with EOCA had abnormality of at least one of the EP parameters. Brainstem auditory evoked response (BAER) studies were abnormal in 50, followed by abnormalities in posterior tibial somatosensory evoked potential (SSEP) (46.1), visual evoked potential (VEP) and median SSEP (30.8 each). Only the abnormality of posterior tibial SSEP had a positive correlation with the duration of disease. The abnormalities in SSEP were more frequent in EOCA than in OPCA and were comparable to that of FA patients. On the contrary, abnormalities of VEP and BAER in EOCA patients were significantly less common (especially VEP) than in FA patients and were almost comparable to OPCA. Thus, on the basis of conventional evoked potential studies, EOCA patients seem to share some common features of FA and OPCA patients. There was no single EP feature to characterize EOCA as a distinct entity.






[PDF Not available]*


        
Print this article     Email this article

Online since 20th March '04
Published by Wolters Kluwer - Medknow