Neurol India Close
 

Figure 6: A 9-year-old boy (a) presented with gelastic seizures and precocious puberty (as evidenced by the growth of secondary sexual characteristics) and (b) supernumerary finger. His luteinizing hormone/follicle-stimulating hormone was raised. His testosterone levels were very high (711 ug/ml). Magnetic resonance imaging (MRI) (c and d) showed a Type III hypothalamic hamartoma attached to the left side of third ventricle and the floor. An endoscopic disconnection was planned. Since the lesion was arising from the left ventricular wall, it was decided to approach the lesion from the right side as the axis of vision would be along the plane of disconnection (d and e). A neuronavigation-guided endoscopic disconnection was performed through a right posterior frontal burr hole (f). Following surgery, the hormones reduced significantly. He was, in addition, started on chemotherapy. Postoperative MRI (g) showed an adequate disconnection

Figure 6: A 9-year-old boy (a) presented with gelastic seizures and precocious puberty (as evidenced by the growth of secondary sexual characteristics) and (b) supernumerary finger. His luteinizing hormone/follicle-stimulating hormone was raised. His testosterone levels were very high (711 ug/ml). Magnetic resonance imaging (MRI) (c and d) showed a Type III hypothalamic hamartoma attached to the left side of third ventricle and the floor. An endoscopic disconnection was planned. Since the lesion was arising from the left ventricular wall, it was decided to approach the lesion from the right side as the axis of vision would be along the plane of disconnection (d and e). A neuronavigation-guided endoscopic disconnection was performed through a right posterior frontal burr hole (f). Following surgery, the hormones reduced significantly. He was, in addition, started on chemotherapy. Postoperative MRI (g) showed an adequate disconnection